Received October 28, 2020
Accepted April 28, 2021

Congenital abnormalities of the uterus mainly result from embryological maldevelopment of the paramesonephric ducts and have been associated with pregnancy complications, reduced fertility and other adverse fetal outcomes. While such abnormalities are rare, affected patients should be correctly managed to improve psychological, sexual, and reproductive outcomes. This review intends to elucidate the impact of congenital uterine abnormalities on fertility and pregnancy outcomes. We also present the available management methods and discuss the role of assisted reproductive technologies (ART) to benefit affected women. This review clearly shows that although these disorders are generally not lethal, they critically impact the patient’s reproductive health. Fertility rate of patients with uterine congenital abnormalities depends on the severity of the condition. Reproductive endocrinologists and infertility specialists must be considered as active parts of the interdisciplinary treatment team for such patients. The ART practices are reasonably successful in managing fertility problems of women with these abnormalities.