Table 1. MEN1 syndrome - key clinical features of (adapted from Hoff, Hauache, 2005).
Syndrome Key clinical features Genetics
MEN1 Pituitary adenoma Loss of function inMEN1-encoded menin protein (11q13)
  Primaryhyperparathyroidism  
  Pancreaticislettumors  
  Adrenals tumors  
  Cutaneousangiofibromas  
  Lipomas